Primary lymphangiectasia of the gastrointestinal tract


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Abstract

Intestinal lymphangiectasia is a very rare pathology, characterized by the presence of enlarged lymphatic vessels in all layers of the intestinal wall and in the mesentery. As a result, "lymphatic lakes" are formed, through which lymph exudates into the lumen of the intestine. The main manifestation is hypoproteinemic edema. Diagnosis of the disease is based on laboratory-instrumental methods of investigation, including by determining in the stool α-1 antitrypsin as a screening test. Treatment includes: a diet rich in calcium, trace elements, be sure to use medicinal foods enriched with medium chain triglycerides, substitution and symptomatic therapy.

About the authors

E M Esedov

FSBEI HE "Dagestan State Medical University" Ministry of Health

проф, д.м.н., зав. каф. госпитальной терапии №2 Makhachkala, Russia

A S Abasova

FSBEI HE "Dagestan State Medical University" Ministry of Health

Email: albinadgma@mail.ru
доцент, к.м.н. Makhachkala, Russia

F D Akhmedova

FSBEI HE "Dagestan State Medical University" Ministry of Health

доцент, к.м.н. Makhachkala, Russia

L N Musaeva

FSBEI HE "Dagestan State Medical University" Ministry of Health

клинический ординатор каф. госпитальной терапии №2 Makhachkala, Russia

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