Pityriasis rubra pilaris (Devergie's disease) in a COVID-19 patient

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Abstract

Pityriasis rubra pilaris (Devergie's disease) is an idiopathic, papulosquamous inflammatory dermatosis characterized by progressive erythrodermia. The etiology of the disease is unknown, and most cases occur sporadically. Viral infections, impaired vitamin A metabolism, medications, autoimmune reactions, and malignancies are most common triggering factors. The diagnosis of Devergie's disease is based on the clinical manifestations of the disease and the results of a skin histological examination. The present paper discusses a clinical case of pityriasis rubra pilaris that occurred in a COVID-19, 40-year-old woman. For the purpose of differential diagnosis of pitiriasis with atopic dermatitis, erythrodermic form of psoriasis, generalized form of urticaria, it is necessary to perform immunohistochemical studies to identify the proliferation of immunocompetent cells. Based on the described clinical case, it seems possible to recommend testing for SARS-CoV-2 if a patient has Devergie's disease against the background of fever and intoxication syndrome.

About the authors

Evgenia V. Okladnikova

Krasnoyarsk State Medical University

Email: farmasis@yandex.ru
ORCID iD: 0000-0002-1909-222X
SPIN-code: 1220-9302

MD, Cand. Sci. (Med.), associated professor

Russian Federation, Partizanа Zheleznyakа str., 1, 660022, Krasnoyarsk

Kseniya V. Kotova

Krasnoyarsk State Medical University

Email: ksuhry@mail.ru
ORCID iD: 0000-0001-9868-5017

MD, assistant lecturer

Russian Federation, Partizanа Zheleznyakа str., 1, 660022, Krasnoyarsk

Vladimir Khorzhevskii

Krasnoyarsk State Medical University; Krasnoyarsk Pathological Bureau

Email: vladpatholog@yandex.ru
ORCID iD: 0000-0002-9196-7246

MD, Cand Sci. (Med.)

Russian Federation, Partizanа Zheleznyakа str., 1, 660022, Krasnoyarsk; Partizanа Zheleznyakа str., 3D, 660022, Krasnoyarsk

Tatiana G. Ruksha

Krasnoyarsk State Medical University

Author for correspondence.
Email: tatyana_ruksha@mail.ru
ORCID iD: 0000-0001-8142-4283
SPIN-code: 5412-2148
Scopus Author ID: 23009925600

MD, Dr. Sci. (Med), Professor

Russian Federation, Partizanа Zheleznyakа str., 1, 660022, Krasnoyarsk

References

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Supplementary files

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1. JATS XML
2. Fig. 1. Macular and papular lesions on the upper extremities

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3. Fig. 2. Changes in the epidermis — acanthosis, alternating areas of para- and orthokeratosis, perifollicular parakeratosis, staining by hematoxilyn and eosin, ×100

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4. Fig. 3. Perivascular lymphoid dermal infiltrate, staining by hematoxilyn and eosin, ×200

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5. Fig. 4. Civatte bodies presence in epidermis, staining by hematoxilyn and eosin, ×200

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6. Fig. 5. Ki-67 immunovisualization in affected skin, ×100

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7. Fig. 6. CD4+ cells immunovisualization, ×100

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8. Fig. 7. CD8+ cells immunovisualization, ×100

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9. Fig. 8. Immunostaining by anti-CD20 antibodies, ×100

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Copyright (c) 2022 Okladnikova E.V., Kotova K.V., Khorzhevskii V., Ruksha T.G.

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