On the classification of spondylometaphyseal dysplasias: spondylophysial-metaphyseal dysplasia

A clinical and radiological analysis of 107 cases of hereditary systemic diseases of the skeleton with a predominant lesion of the germ (fizar) and metaphyseal zones, which are combined into the group "spondylophysial-metaphyseal dysplasia", was carried out. Changes in the skeleton were traced in dynamics, the age of the observed patients was from 1 to 16 years. Three types of spondylophysial-metaphyseal dysplasia have been identified, depending on the degree of damage to the fizar and metaphyseal zones and its predominant localization: A (with a predominant lesion of the hip joints), B (with a predominant lesion of the spine) and C (with a uniform lesion of the spine and long bones)