VACTERL ASSOCIATION OF INBORN BIRTH DEFECTS - A SURGEON’S OPINION
- Authors: Kozlov Y.A.1,2,3, Kovalkov K.A.4, Chubko D.M.5, Baradieva P.Z.1, Timofeev A.D.2, Zvonkov D.A.2, Us G.P.1,2,3,4,5, Kuznetsova N.N.1,2,3,4,5
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Affiliations:
- Municipal Ivano-Matryona Children’s Clinical Hospital
- Irkutsk State Medical University
- Irkutsk State Medical Academy of Postgraduation
- Children’s Municipal Clinical Hospital No. 5
- Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection
- Issue: Vol 6, No 3 (2016)
- Pages: 95-101
- Section: Reviews
- URL: https://journal-vniispk.ru/2219-4061/article/view/122709
- DOI: https://doi.org/10.17816/psaic277
- ID: 122709
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Full Text
Abstract
VACTERL association is a set of certain abnormalities in one newborn which include defects of the esophagus, rectum, heart, kidneys, vertebral column and extremities. Research papers devoted to the study of this complex disease are still rare. The majority of researchers insist that the syndrome was composed at least of three components (abnormalities of vertebra, tracheoesophageal fistula and anal atresia) though others believe that the constituents of VACTERL are constant. Treatment of the syndrome is usually restricted by surgeries which are needed to restore the esophagus, anus, eliminate abnormalities of the cardiovascular and excretory system and extremities. The scientific research is devoted to the study of VACTERL, correct interpretation of its components, determination of knowledge weaknesses and description of modern therapeutic approaches intended for the correction of surgical abnormalities included into the syndrome.
About the authors
Yu. A. Kozlov
Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation
Author for correspondence.
Email: noemail@neicon.ru
Russian Federation
K. A. Kovalkov
Children’s Municipal Clinical Hospital No. 5
Email: noemail@neicon.ru
Russian Federation
D. M. Chubko
Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection
Email: noemail@neicon.ru
Russian Federation
P. Zh. Baradieva
Municipal Ivano-Matryona Children’s Clinical Hospital
Email: noemail@neicon.ru
Russian Federation
A. D. Timofeev
Irkutsk State Medical University
Email: noemail@neicon.ru
Russian Federation
D. A. Zvonkov
Irkutsk State Medical University
Email: noemail@neicon.ru
Russian Federation
G. P. Us
Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection
Email: noemail@neicon.ru
Russian Federation
N. N. Kuznetsova
Municipal Ivano-Matryona Children’s Clinical Hospital; Irkutsk State Medical University; Irkutsk State Medical Academy of Postgraduation; Children’s Municipal Clinical Hospital No. 5; Krasnoyarsk Regional Clinical Centre of Maternity and Childhood Protection
Email: noemail@neicon.ru
Russian Federation
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