A rare case of rectal inflammatory myofibroblastic tumor mimicking Crohn disease in a child
- Authors: Glushkova V.A.1, Shcherbakova O.V.2,3, Gabrusskaya T.V.1, Khabibullina L.R.3, Podkamenev А.V.1, Peredereev S.S.1
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Affiliations:
- Saint Petersburg State Pediatric Medical University
- Federal Scientific and Clinical Center for Children and Adolescents
- Pirogov Russian National Research Medical University
- Issue: Vol 15, No 1 (2025)
- Pages: 109-117
- Section: Case reports
- URL: https://journal-vniispk.ru/2219-4061/article/view/312988
- DOI: https://doi.org/10.17816/psaic1891
- ID: 312988
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Abstract
Inflammatory myofibroblastic tumor is a rare type of mesenchymal tumor, predominantly benign but with intermediate malignant potential. This article presents a clinical case of successful surgical treatment of a child with an extremely rare localization of inflammatory myofibroblastic tumor in the rectum (the fourth reported case worldwide), initially misdiagnosed as Crohn disease. A 4-year-old girl presented with diarrhea, blood, and mucus in stool. Examination revealed ulcerative pancolitis and a rectal mass, initially presumed to be of inflammatory origin. Treatment with mesalazine led to clinical improvement; however, follow-up endoscopy showed no significant regression. Therapy was escalated to topical and systemic budesonide, with a positive response, but symptoms recurred after glucocorticoid withdrawal, including ribbon-like feces and painful defecation. High fecal calprotectin levels persisted throughout the observation period. The condition was interpreted as a stricturing form of Crohn disease. Anti-TNF therapy (infliximab) initially led to clinical improvement, but the rectal mass continued to grow, with progressive anal canal stenosis. A decision was made to perform rectal resection with tumor excision. Histopathological examination confirmed the diagnosis of inflammatory myofibroblastic tumor. Due to the overlapping clinical, laboratory, and imaging features of inflammatory myofibroblastic tumor and Crohn disease, differential diagnosis can be challenging, potentially delaying accurate diagnosis. In this case, a child with an extremely rare localization of an inflammatory myofibroblastic tumor successfully underwent radical surgery, resulting in favorable long-term outcomes.
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##article.viewOnOriginalSite##About the authors
Victoria A. Glushkova
Saint Petersburg State Pediatric Medical University
Author for correspondence.
Email: pedsurgspb@yandex.ru
ORCID iD: 0009-0002-4768-1539
SPIN-code: 8703-3966
Russian Federation, Saint Petersburg
Olga V. Shcherbakova
Federal Scientific and Clinical Center for Children and Adolescents; Pirogov Russian National Research Medical University
Email: Shcherbakovaov@kidsfmba.ru
ORCID iD: 0000-0002-8514-3080
SPIN-code: 3478-8606
Russian Children’s Clinical Hospital, MD, Dr. Sci. (Medicine)
Russian Federation, Moscow; MoscowTatyana V. Gabrusskaya
Saint Petersburg State Pediatric Medical University
Email: tatyanagabrusskaya@yandex.ru
ORCID iD: 0000-0002-7931-2263
SPIN-code: 2853-5956
MD, Cand. Sci. (Medicine), Assistant Professor
Russian Federation, Saint PetersburgLinara R. Khabibullina
Pirogov Russian National Research Medical University
Email: Habibull.lin@yandex.ru
ORCID iD: 0000-0002-1515-0699
SPIN-code: 7241-8029
Russian Children’s Clinical Hospital
Russian Federation, MoscowАleksey V. Podkamenev
Saint Petersburg State Pediatric Medical University
Email: av.podkamenev@gpmu.org
ORCID iD: 0000-0001-6006-9112
SPIN-code: 7052-0205
MD, Dr. Sci. (Medicine), Assistant Professor
Russian Federation, Saint PetersburgSergey S. Peredereev
Saint Petersburg State Pediatric Medical University
Email: speredereev@yandex.ru
ORCID iD: 0000-0002-9380-8150
SPIN-code: 6046-6407
MD, Cand. Sci. (Medicine)
Russian Federation, Saint PetersburgReferences
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